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KMID : 0358420140570050409
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Korean Journal of Obstetrics and Gynecology
2014 Volume.57 No. 5 p.409 ~ p.411
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A 6-year-old girl with vaginal spotting who was diagnosed with perivascular epithelioid cell neoplasm after vaginoscopic resection
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Cho Hyun-Jung
Lee Mi-Kyung
Kang Byung-Moon
Kim Sung-Hoon
Chae Hee-Dong
Kim Chung-Hoon
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Abstract
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Perivascular epithelioid cell neoplasm (PEComa) is a rare tumor with unknown malignant potential. We report a case of a 6-year-old child with history of brain tumor (pineoblastoma), who presented with intermittent vaginal spotting for 6 months. A vaginoscopy revealed a 1.5×1.0-cm mass on the vaginal wall. Pathological examination demonstrated that the tumor was composed of clear cells with organoid patterns, which were immunohistochemically positive for HMB-45 and TFE3, and negative for CK, HNF1-B, SOX10, Melan A, and S-100 protein. These findings were consistent with PEComa arising from the vagina. Regular follow-up with magnetic resonance imaging has shown no signs of recurrence. This case shows that early detection of PEComa and subsequent regular follow-ups are important because of the neoplasm’s unknown malignant potential.
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KEYWORD
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Perivascular epithelioid cell neoplasms, Resection, Vagina, Vaginoscopy
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